Karya
Judul/Title Outcomes of children with long-segment and total colon Hirschsprung disease following pull-through
Penulis/Author ASTRI KHAIRANA WARDHANI (1); Krisna Dwiantama (2); dr. Kristy Iskandar, M.Sc, Ph.D, Sp.A. Subsp.Neuro.(K) (3); dr. Junaedy Yunus, M.Sc., Ph.D. (4); Prof. dr. Gunadi, Ph.D, Sp.BA., Subsp.DA(K) (5)
Tanggal/Date 2024
Kata Kunci/Keyword
Abstrak/Abstract Introduction: Hirschsprung disease (HSCR) is a congenital disorder caused by the absence of ganglion cells, which leads to a functional obstruction in infants. HSCR is divided into short, long and total colon aganglionosis (TCA). However, post-operative outcome assessment of patients with long-segment and TCA is scarce. We determined the functional outcomes, Hirschsprung-associated enterocolitis (HAEC) and complications of long-segment and TCA HSCR’s children following pull-through surgery. Materials and Methods: Descriptive analysis research was done for children with HSCR long-segment and TCA who underwent an operation at our institutionfrom 2013 to 2020. We assessed the functional outcome and HAEC by the Krickenbeck and the HAEC scoring, respectively. Results: We ascertained 13 HSCR long-segment and six TCA. We performed the following surgical procedures: Duhamel (n=7), Martin (n=4), Kimura (n=1), transabdominal Yancey-Soave (n=3) and transanal endorectal pull-through (n=4). All long-segment patients revealed good functional outcomes, whereas two TCA children suffered soiling and failed to achieve voluntary bowel movement. HAEC was noted in three long-segment and four TCA patients. Furthermore, surgical site infection and diaper rash were noticed in 10 and two patients, respectively. Conclusion: Long-segment patients might have better functional outcomes TCA group, whereas the frequency of HAEC is compatible among arms. Long-term follow-up is important and necessary to identify complications early and define the proper treatment. Our study comprehensively analyzes functional outcomes, HAEC and complications of children with HSCR long-segment and TCA after definitive surgery in a developing country.
Rumpun Ilmu Bedah (Umum, Plastik, Orthopaedi, Urologi, Dll)
Bahasa Asli/Original Language English
Level Internasional
Status
Dokumen Karya
No Judul Tipe Dokumen Aksi
12024_OutcomesLongTCA_Astri.pdf[PAK] Full Dokumen
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