| Abstrak/Abstract |
Cherubism is an autosomal dominant disease that causes abnormal osteoblast-osteoclast function, resulting in progressive enlargement around the maxillofacial area due to replacement of normal bone with fibrous tissue and immature bone. Clinical and radiographic signs of cherubism bilateral radiolucent multi-ocular lesions of the mandible and maxilla, causing bilateral cheek swelling. A 9-year-old boy came to the Oral Surgery of Sardjito Hospital, Yogyakarta, with complaints of enlargement of both cheeks nine months ago. The patient complained that the swelling on the maxilla was enlarged and felt disturbing in appearance. The enlargement was painless, not easy to bleed, hard, and disturbing when eating and sleeping. Radiograph examination demonstrated bilateral maxillary and mandibular multi-ocular-radiolucent lesions. Three stages of surgery were performed: biopsy-incision with histopathological results; benign fibrous histiocytoma, curettage-reshaping of the mandible 1 month after biopsy, and curettage-reshaping of the maxilla 9 months after mandible surgery. The histopathological results of the lesions in the maxilla and mandible showed the same results: peripheral reparative giant cell granuloma. Twelve months postoperatively, the patient had no complaints, no disturbances in eating and sleeping, symmetrical face. The patient's initial curettage and reshaping resolved masticatory complaints, improved facial aesthetics, and reduced lesions' expansion at the bilateral mandibular and maxillary bones. |
